Celine Dion reveals she is suffering from ‘very rare’ and incurable stiff-person syndrome
Celine Dion has revealed she is suffering from stiff-person syndrome, an incurable and rare neurological disorder which causes muscle stiffness and spasms
The Canadian star gave details of her condition in an emotional video message to fans, saying she is suffering spasms “that affect every aspect” of her life, causing difficulty when she walks and preventing her from using her vocal chords properly.
Dion, known for her hit power ballads including Think Twice, Because You Loved Me, My Heart Will Go On, and It’s All Coming Back To Me Now, delayed a Las Vegas residency in 2021 and postponed tour dates earlier this year due to health issues.
Pic: AP
In her video message, the singer said she now has no choice but to postpone most of her European shows, originally planned to start in February 2023, until 2024. Some shows, including dates in Greece and Romania, have been cancelled altogether.
“As you know, I’ve always been an open book and I wasn’t ready to say anything before, but I’m ready now,” Dion said.
“I’ve been dealing with problems with my health for a long time and it’s been really difficult for me to face these challenges and to talk about everything that I’ve been going through.
“Recently I’ve been diagnosed with a very rare neurological disorder called stiff person syndrome, which effects something like one in a million people.
“While we are still learning about this rare condition we now know this is what’s been causing all of the spasms I’ve been having.
“Unfortunately these spasms affect every aspect of my daily life, sometimes causing difficulties when I walk and not allowing me to use my vocal chords to sing the way I’m used to.”
Dion appeared tearful during her message, which she recorded in English and French, telling fans that it “hurts” to say she will not be ready to restart her European tour, which included UK dates, in February, and that she misses performing.
‘All I know is singing… I miss you so much’
“I have a great team of doctors working alongside me to help me get better, and my precious children who are supporting me and giving me hope,” she said. “I’m working hard with my sports medicine therapist every day to build back my strength and my ability to perform again, but I have to admit it’s been a struggle.
“All I know is singing, it’s what I’ve done all my life and it’s what I love to do the most. I miss you so much, I miss seeing all of you, being on the stage, performing for you. I always give 100% when I do my shows but my condition is not allowing me to give you that right now.”
Dion said she has no choice but to concentrate on her health and is hopeful that she is “on the road to recovery”.
She finished by saying: “This is my focus and I’m doing everything that I can to recuperate. I want to thank you so much for your encouraging wishes of love and support on my social media. This means a lot to me. Take care of yourselves, be well. I love you guys so much. And I really hope I can see you again real soon.”
What is stiff-person syndrome?
According to the National Institute of Neurological Disorders and Stroke in the US, stiff-person syndrome (SPS) is a rare neurological disorder with features of an autoimmune disease.
On its website, the institute says that SPS is characterised by “fluctuating muscle rigidity in the trunk and limbs and a heightened sensitivity to stimuli such as noise, touch, and emotional distress, which can set off muscle spasms…
“Abnormal postures, often hunched over and stiffened, are characteristic of the disorder. People with SPS can be too disabled to walk or move, or they are afraid to leave the house because street noises, such as the sound of a horn, can trigger spasms and falls.”
It says the disease affects twice as many women as men and that “scientists don’t yet understand what causes SPS, but research indicates that it is the result of an autoimmune response gone awry in the brain and spinal cord”.
Entertainment
Googlebox star George Gilbey’s mum reveals his last words to her before he fell to his death
The mother of Gogglebox star George Gilbey has revealed his last words to her were “I love you”.
Gilbey died after falling through a plastic skylight while fixing a warehouse roof in Essex in March.
The 40-year-old appeared alongside his mum, Linda McGarry, and stepdad on the hit Channel 4 show.
The family first appeared on the second series of Gogglebox in 2013 but were dropped the following year when Gilbey signed up for the 14th series of Celebrity Big Brother in 2014, reaching the final.
Mrs McGarry said she spoke to him on the phone hours before his death.
Gilbey appeared alongside his mum Linda and stepdad Pete on Gogglebox. Pic: PA
She told The Sun: “He phoned me at 9.30 in the morning and said he was working – and asked me for his ‘breakfast money’.
“I put £30 in his account so he could get food, and he seemed fine.
“He had a drink the night before, and liked a bottle of white wine or two, but was happy that he was working. He ended the phone call by saying, ‘I love you’ like he usually did. I treasure those words.”
She added: “It was an honour for him to have been my son. We had a blast for 40 years.”
Mrs McGarry said her son had struggled with the death of his dad, stepfather and her own Parkinson’s diagnosis.
At the time of his death, he was working to save money to move closer to his seven-year-old daughter, Amelie, in southwest London.
“He wanted to be with Amelie, who he adored,” she told The Sun.
“They were on the third day of a job that was going to last a month, and he was going to get money together from that.
“When they were together, George and Amelie were always laughing. She is going to miss him terribly, like we all will.”
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Gilbey suffered traumatic injuries to his head and torso and died at the scene in Shoeburyness.
An inquest was opened last week but suspended after a request from police pending a criminal investigation.
A man in his 40s from the Witham area of Essex was previously arrested on suspicion of gross negligence manslaughter
He was later released under investigation.
Entertainment
Bestselling author CJ Sansom dies days before Disney adaption of his Shardlake series airs
Author CJ Sansom, who created the character of Matthew Shardlake, has died at the age of 71, his publisher has announced.
Sansom first introduced readers to Shardlake – a lawyer who solves crimes while navigating the religious reforms and political intrigue of Tudor England – in the 2003 book Dissolution.
The Scottish writer released six further novels featuring Shardlake, as well as two standalone historical novels, Winter In Madrid and Dominion.
His works have just been adapted into the series Shardlake, which features The Innocents star Arthur Hughes as the main character and Game Of Thrones actor Sean Bean as Thomas Cromwell.
The first season of the Tudor murder mystery series is set to be released by Disney+ on Wednesday.
Sansom was described as one of Britain’s best historical novelists. Pic: Pan Macmillian/PA
Announcing his death on Monday, publishers Pan Macmillan wrote in a statement: “It is with immense sadness that Pan Macmillan announces the death of CJ Sansom.”
“‘It is an extraordinarily strange coincidence that Chris has died only a handful of days before a new generation of fans will meet Matthew Shardlake, Barak and Guy and co for the first time through,” his agent, Antony Topping, said.
“This is also a moment for which Chris’s established fans have been waiting a long time.
“Chris was so proud of all the work and determination that went into bringing the novels to our television screens, which I hope will bring an entirely new audience to the books and which will maybe also inspire some old fans to return to their favourite CJ Sansom novels.”
Sansom’s long-time editor and publisher, Maria Rejt, added that he was working on a new Shardlake book but his “worsening health made progress painfully slow”.
Arthur Hughes as protagonist Matthew Shardlake. Pic: Disney+ UK
She described the author as an “intensely private person” who took immense pleasure in the public’s enthusiastic response to his novels.
“I shall miss him hugely, not only as a wonderfully talented writer who gave joy to millions, but as a dear friend of enormous compassion and integrity,” Ms Rejt said.
Shardlake featured as the protagonist in a total of seven of Sansom’s novels. Dissolution was dramatised once before by BBC Radio 4 in 2012.
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Sean Bean stars in the new series based off Sansom’s debut novel. Pic: Disney+ UK
With more than three million copies of his novels in print, Sansom was awarded the Crime Writers’ Association Cartier Diamond Dagger Award in 2022 for his outstanding contribution to the genre.
Born in Edinburgh in 1952, Sansom attended Birmingham University where he studied an undergraduate degree and PhD in history.
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He worked as a solicitor before becoming a full-time writer where he was able to combine his passion for history and law securing him as one of Britain’s bestselling historical novelists.
Sansom was also a signatory to an 2014 open letter advocating that Scotland should remain in the UK.
The author also donated £161,000 to the Better Together campaign, according to published accounts.
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